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- W2734516627 abstract "Patients with pulmonary arterial hypertension associated with connective tissue disease (PAH‐PAH‐CTD) such as systemic sclerosis (SSc) have a poorer response to treatment and increased mortality compared with patients with idiopathic PAH. Current treatment options for PAH‐CTD include prostanoids, phosphodiesterase type‐5 inhibitors (PDE‐5i), endothelin receptor antagonists, and the soluble guanylate cyclase stimulator riociguat. In this case series, we describe three patients with PAH‐CTD related to limited scleroderma who were switched from a PDE‐5i to riociguat due to insufficient clinical response. The switch to riociguat was associated with an improvement in respiratory and hemodynamic parameters and a favorable tolerability profile. These cases demonstrate that switching to riociguat is a therapeutic option in patients with PAH‐CTD who have not achieved a satisfactory clinical response to a PDE‐5i." @default.
- W2734516627 created "2017-07-21" @default.
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- W2734516627 date "2017-07-01" @default.
- W2734516627 modified "2023-09-24" @default.
- W2734516627 title "Replacing a phosphodiesterase‐5 inhibitor with riociguat in patients with connective tissue disease‐associated pulmonary arterial hypertension: a case series" @default.
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- W2734516627 doi "https://doi.org/10.1177/2045893217721694" @default.
- W2734516627 hasPubMedCentralId "https://www.ncbi.nlm.nih.gov/pmc/articles/5841890" @default.
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