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- W2741627992 endingPage "476" @default.
- W2741627992 startingPage "463" @default.
- W2741627992 abstract "Abstract Löfgren's syndrome (LS), first described in 1946 by Swedish Professor of Medicine Sven Löfgren, is a clinically distinct phenotype of sarcoidosis. Patients typically experience an acute disease onset, usually with fever, and characteristic symptoms of bilateral hilar lymphadenopathy, erythema nodosum, and/or bilateral ankle arthritis or periarticular inflammation. LS patients are well documented to have a good prognosis, which is especially true for HLA-DRB1*03+ individuals. The presence of this allele correlates closely with an accumulation of clonal CD4+ T-cell populations in the lung, suggestive of local antigen recognition. Moreover, LS differs markedly from “non-LS” sarcoidosis regarding immune cell activation, differentiation, and regulation, which may influence clinical outcome and spontaneous disease resolution. This review offers an overview of the clinical characteristics, genetic background, and immunological characteristics of LS, as well as patient management, and reflections on future scientific challenges, emphasizing the concept of LS as a disease in its own right." @default.
- W2741627992 created "2017-08-08" @default.
- W2741627992 creator A5000843678 @default.
- W2741627992 creator A5009140932 @default.
- W2741627992 creator A5039613036 @default.
- W2741627992 creator A5061442564 @default.
- W2741627992 date "2017-07-27" @default.
- W2741627992 modified "2023-10-02" @default.
- W2741627992 title "Löfgren's Syndrome: Diagnosis, Management, and Disease Pathogenesis" @default.
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