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- W2768138587 abstract "<ns4:p>Idiopathic pulmonary fibrosis (IPF) is a rare pulmonary disease with a poor prognosis and severe impact on quality of life. Early diagnosis is still challenging and important delays are registered before final diagnosis can be reached. Available tools fail to predict the variable course of the disease and to evaluate response to antifibrotic drugs. Despite the recent approval of pirfenidone and nintedanib, significant challenges remain to improve prognosis and quality of life. It is hoped that the new insights gained in pathobiology in the last few years will lead to further advances in the diagnosis and management of IPF. Currently, early diagnosis and prompt initiation of treatments reducing lung function loss offer the best hope for improved outcomes. This article aims at providing an overview of recent advances in managing patients with IPF and has a particular focus on how to reach a diagnosis, manage comorbidities and lung transplantation, care for the non-pharmacological needs of patients, and address palliative care.</ns4:p>" @default.
- W2768138587 created "2017-12-04" @default.
- W2768138587 creator A5002649308 @default.
- W2768138587 creator A5017716537 @default.
- W2768138587 date "2017-11-27" @default.
- W2768138587 modified "2023-09-24" @default.
- W2768138587 title "Recent advances in managing idiopathic pulmonary fibrosis" @default.
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- W2768138587 doi "https://doi.org/10.12688/f1000research.10720.1" @default.
- W2768138587 hasPubMedCentralId "https://www.ncbi.nlm.nih.gov/pmc/articles/5710314" @default.
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- W2768138587 hasPublicationYear "2017" @default.
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