Matches in SemOpenAlex for { <https://semopenalex.org/work/W2771753911> ?p ?o ?g. }
- W2771753911 endingPage "192" @default.
- W2771753911 startingPage "173" @default.
- W2771753911 abstract "Abstract The striated muscle cell cytoskeleton is a multifunctional, dynamic, and complex structure that serves as a scaffold to maintain the structural integrity and architecture of the cell. However, it also functions as a platform for inter- and intracellular signaling, linking the contractile apparatus so that sarcomeres may function in concert, and linking those structures in turn to the sarcolemma, cell–cell junctions, the mitochondria, and nucleus. This review focuses on the intermediate filament and associated protein components of the cytoskeleton and explores how mutations in desmin lead to cardiomyopathy. The clinical and pathological features of these myopathies are described with a particular focus on placing these events within the broader context of proteotoxicity and its relevance as a converging pathway in cardiac disease." @default.
- W2771753911 created "2017-12-22" @default.
- W2771753911 creator A5005272366 @default.
- W2771753911 date "2017-01-01" @default.
- W2771753911 modified "2023-09-25" @default.
- W2771753911 title "Diseases of the Cytoskeleton" @default.
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