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- W280781636 startingPage "133" @default.
- W280781636 abstract "先证者(Ⅲ2) 女,30岁,20天前无明显诱因出现头晕、头痛,以右后枕部为著,程度中等,发作性,偶伴恶心,无明显呕吐.走路不稳,无发热、抽搐、无肢体麻木、乏力,无视物不清,Rormberg 征阳性,闭目难立征阳性,步态不稳,四肢肌力Ⅳ级.实验室检查:WBC 5.96×109/L,脑脊液WBC 0.002×109/L,渗透压正常. MRI示左侧小脑半球类圆形长T1长T2信号区,呈囊性,大小约5 cm×4 cm×3 cm,四脑室受压前移,后壁见一等信号结节,强化明显." @default.
- W280781636 created "2016-06-24" @default.
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- W280781636 date "2005-04-10" @default.
- W280781636 modified "2023-09-25" @default.
- W280781636 title "Von Hippel-Lindau综合征一家系" @default.
- W280781636 hasPublicationYear "2005" @default.
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