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- W285043201 abstract "症例は40歳,女性.倦怠感,手指腫脹を主訴に某年8月当院受診した.精査目的に入院しMCTDの基準を満たしたため,プレドニゾロン(PSL)40 mg/日の投与を開始した.治療反応性良好であったが発熱,汎血球減少,肝機能障害,フェリチン上昇が出現,骨髄生検でHPSの診断に至った.当初原病に伴うHPSと考えたが,血中HHV-6 DNA値の上昇が判明し,HHV-6の再活性化によりHPSを発症したと判断した.ガンシクロビル投与とPSLの減量で病態は改善した.膠原病治療中に発症したHPSの原因として潜在性のHHV-6再活性化も考慮する必要がある." @default.
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- W285043201 date "2014-01-01" @default.
- W285043201 modified "2023-09-27" @default.
- W285043201 title "A Case of Adult Human Herpes Virus-6 Associated Hemophagocytic Syndrome with Mixed Connective Tissue Disease" @default.
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- W285043201 doi "https://doi.org/10.2169/naika.103.2571" @default.
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