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- W2890870344 abstract "Anti-glomerular basement membrane (anti-GBM) disease is a rare autoimmune small vessel vasculitis characterized by autoreactivity to antigens in type IV collagen chains expressed in glomerular and alveolar basement membrane. The detection of circulating anti-GBM antibodies, which are shown to be directly pathogenic, is central to disease diagnosis. Clinically, anti-GBM disease usually presents with rapidly progressive glomerulonephritis with or without alveolar hemorrhage. Rapid diagnosis and early treatment are required to prevent mortality and to preserve renal function. Relapse in anti-GBM disease is uncommon. Variant and atypical forms of anti-GBM disease are increasingly recognised." @default.
- W2890870344 created "2018-09-27" @default.
- W2890870344 creator A5021272525 @default.
- W2890870344 creator A5025432384 @default.
- W2890870344 date "2018-11-01" @default.
- W2890870344 modified "2023-09-30" @default.
- W2890870344 title "Anti–Glomerular Basement Membrane Disease" @default.
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- W2890870344 doi "https://doi.org/10.1016/j.rdc.2018.06.011" @default.
- W2890870344 hasPubMedId "https://pubmed.ncbi.nlm.nih.gov/30274629" @default.
- W2890870344 hasPublicationYear "2018" @default.
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