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- W2890992227 endingPage "291" @default.
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- W2890992227 abstract "Duchenne’s muscular dystrophy is an X-linked neuromuscular disease that manifests as muscle atrophy and cardiomyopathy in young boys. However, a considerable percentage of carrier females are often diagnosed with cardiomyopathy at an advanced stage. Existing therapy is not disease-specific and has limited effect, thus many patients and symptomatic carrier females prematurely die due to heart failure. Early detection is one of the major challenges that muscular dystrophy patients, carrier females, family members and, research and medical teams face in the complex course of dystrophic cardiomyopathy management. Despite the widespread adoption of advanced imaging modalities such as cardiac magnetic resonance, there is much scope for refining the diagnosis and treatment of dystrophic cardiomyopathy. This comprehensive review will focus on the pertinent clinical aspects of cardiac disease in muscular dystrophy while also providing a detailed consideration of the known and developing concepts in the pathophysiology of muscular dystrophy and forthcoming therapeutic options." @default.
- W2890992227 created "2018-09-27" @default.
- W2890992227 creator A5005043707 @default.
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- W2890992227 creator A5076660483 @default.
- W2890992227 creator A5079534687 @default.
- W2890992227 date "2018-09-19" @default.
- W2890992227 modified "2023-10-03" @default.
- W2890992227 title "Dystrophin Cardiomyopathies: Clinical Management, Molecular Pathogenesis and Evolution towards Precision Medicine" @default.
- W2890992227 cites W1153501715 @default.
- W2890992227 cites W1429841006 @default.
- W2890992227 cites W1519383882 @default.
- W2890992227 cites W1569858236 @default.
- W2890992227 cites W1584198130 @default.
- W2890992227 cites W1584209487 @default.
- W2890992227 cites W1598673059 @default.
- W2890992227 cites W1657080278 @default.
- W2890992227 cites W1757005076 @default.
- W2890992227 cites W1850477203 @default.
- W2890992227 cites W1921003156 @default.
- W2890992227 cites W1926031445 @default.
- W2890992227 cites W1936484224 @default.
- W2890992227 cites W1964137685 @default.
- W2890992227 cites W1966786218 @default.
- W2890992227 cites W1967261851 @default.
- W2890992227 cites W1967746676 @default.
- W2890992227 cites W1968334304 @default.
- W2890992227 cites W1968543820 @default.
- W2890992227 cites W1969570221 @default.
- W2890992227 cites W1971143219 @default.
- W2890992227 cites W1973803913 @default.
- W2890992227 cites W1973879435 @default.
- W2890992227 cites W1977394169 @default.
- W2890992227 cites W1979378760 @default.
- W2890992227 cites W1980142871 @default.
- W2890992227 cites W1983711895 @default.
- W2890992227 cites W1983802385 @default.
- W2890992227 cites W1985119695 @default.
- W2890992227 cites W1985454225 @default.
- W2890992227 cites W1988749764 @default.
- W2890992227 cites W1990234504 @default.
- W2890992227 cites W1990590627 @default.
- W2890992227 cites W1990897270 @default.
- W2890992227 cites W1991248271 @default.
- W2890992227 cites W1991540624 @default.
- W2890992227 cites W1996575615 @default.
- W2890992227 cites W1996860050 @default.
- W2890992227 cites W1997089606 @default.
- W2890992227 cites W1997224266 @default.
- W2890992227 cites W1999826382 @default.
- W2890992227 cites W2000168224 @default.
- W2890992227 cites W2002426309 @default.
- W2890992227 cites W2003247108 @default.
- W2890992227 cites W2004510106 @default.
- W2890992227 cites W2004824383 @default.
- W2890992227 cites W2005061403 @default.
- W2890992227 cites W2005245653 @default.
- W2890992227 cites W2005586230 @default.
- W2890992227 cites W2005703297 @default.
- W2890992227 cites W2007123925 @default.
- W2890992227 cites W2007398635 @default.
- W2890992227 cites W2009167881 @default.
- W2890992227 cites W2012912755 @default.
- W2890992227 cites W2013319031 @default.
- W2890992227 cites W2013621644 @default.
- W2890992227 cites W2014537162 @default.
- W2890992227 cites W2015870495 @default.
- W2890992227 cites W2016615191 @default.
- W2890992227 cites W2016965630 @default.
- W2890992227 cites W2018358939 @default.
- W2890992227 cites W2018528089 @default.
- W2890992227 cites W2018862827 @default.
- W2890992227 cites W2019428638 @default.
- W2890992227 cites W2019563312 @default.
- W2890992227 cites W2021269902 @default.
- W2890992227 cites W2023228563 @default.
- W2890992227 cites W2025314206 @default.
- W2890992227 cites W2027522871 @default.
- W2890992227 cites W2029158145 @default.
- W2890992227 cites W2029914169 @default.
- W2890992227 cites W2033924360 @default.
- W2890992227 cites W2035051422 @default.
- W2890992227 cites W2035105610 @default.
- W2890992227 cites W2035312069 @default.
- W2890992227 cites W2035975703 @default.
- W2890992227 cites W2037638857 @default.
- W2890992227 cites W2038685361 @default.
- W2890992227 cites W2039752944 @default.
- W2890992227 cites W2042898299 @default.