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- W2895540017 endingPage "3063" @default.
- W2895540017 startingPage "3063" @default.
- W2895540017 abstract "Mucopolysaccharidosis (MPS) are a group of lysosomal storage disorders that are caused by the deficiency of enzymes involving in the catabolism of glycosaminoglycan (GAGs). GAGs incompletely degraded accumulate in many sites, damaging tissues and cells, leading to a variety of clinical manifestations. Many of these manifestations are painful, but few data are available in the literature concerning the prevalence, etiology, and pathogenesis of pain in children with MPS. This review, through the analysis of the data available the in literature, underscores the relevant prevalence of pain in MPSs’ children, provides the instruments to discern the etiopathogenesis of the disease and of pain, illustrates the available molecules for the management of pain and the possible advantages of non-pharmacological pain therapy in MPSs’ patients." @default.
- W2895540017 created "2018-10-12" @default.
- W2895540017 creator A5006788728 @default.
- W2895540017 creator A5035735859 @default.
- W2895540017 creator A5043853692 @default.
- W2895540017 creator A5077882643 @default.
- W2895540017 date "2018-10-08" @default.
- W2895540017 modified "2023-09-25" @default.
- W2895540017 title "Pain in Mucopolysaccharidoses: Analysis of the Problem and Possible Treatments" @default.
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