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- W2896054757 endingPage "18" @default.
- W2896054757 startingPage "11" @default.
- W2896054757 abstract "Abstract Systemic sclerosis ( SS c) is a complex autoimmune connective tissue disease combining inflammatory, vasculopathic and fibrotic manifestations. Skin features, which give their name to the disease and are considered as diagnostic as well as prognostic markers, have not been thoroughly investigated in terms of therapeutic targets. CCN proteins ( CYR 61/ CCN 1, CTGF / CCN 2, NOV / CCN 3 and WISP 1‐2‐3 as CCN 4‐5‐6) are a family of secreted matricellular proteins implicated in major cellular processes such as cell growth, migration, differentiation. They have already been implicated in key pathophysiological processes of SS c, namely fibrosis, vasculopathy and inflammation. In this review, we discuss the possible implication of CCN proteins in SS c pathogenesis, with a special focus on skin features, and identify the potential actionable CCN targets." @default.
- W2896054757 created "2018-10-26" @default.
- W2896054757 creator A5008823637 @default.
- W2896054757 creator A5040092699 @default.
- W2896054757 creator A5042296138 @default.
- W2896054757 creator A5077710346 @default.
- W2896054757 creator A5086349143 @default.
- W2896054757 date "2018-12-11" @default.
- W2896054757 modified "2023-10-18" @default.
- W2896054757 title "<scp>CCN</scp> proteins as potential actionable targets in scleroderma" @default.
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