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- W2900996857 abstract "Systemic vasculitides are a group of heterogeneous conditions with overlapping patterns of clinical and laboratory manifestations. Moreover, clinical features can be non-specific and seemingly disparate. A major factor in defining optimal therapy and measuring treatment response is careful disease assessment targeting four main domains: activity, damage, prognosis and quality of life/function. Assessment tools such as the Birmingham Activity Score and the Vasculitis Damage Index have become a core feature of clinical trials in ANCA-associated vasculitis (AAV) and formed the basis for sound clinical management of these complex conditions. We are still lacking accurate definitions of disease activity and damage progression in large-vessel vasculitis. There is an increasing interest in the role of patient-reported outcomes as a measure of disease impact; a disease-specific measure for use in AAV is being validated. We review how best to evaluate patients with large-, medium- and small-vessel vasculitis." @default.
- W2900996857 created "2018-11-29" @default.
- W2900996857 creator A5002804464 @default.
- W2900996857 creator A5005974898 @default.
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- W2900996857 date "2018-02-01" @default.
- W2900996857 modified "2023-10-16" @default.
- W2900996857 title "Clinical features and structured clinical evaluation of vasculitis" @default.
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- W2900996857 doi "https://doi.org/10.1016/j.berh.2018.10.001" @default.
- W2900996857 hasPubMedId "https://pubmed.ncbi.nlm.nih.gov/30526897" @default.
- W2900996857 hasPublicationYear "2018" @default.
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