Matches in SemOpenAlex for { <https://semopenalex.org/work/W2901760304> ?p ?o ?g. }
- W2901760304 abstract "Systemic sclerosis (SSc) is a severe auto-immune disease, characterized by vasculopathy and fibrosis of connective tissues. SSc has a high morbidity and mortality and unfortunately no disease modifying therapy is currently available. A key cell in the pathophysiology of SSc is the myofibroblast. Myofibroblasts are fibroblasts with contractile properties that produce a large amount of pro-fibrotic extracellular matrix molecules such as collagen type I. In this narrative review we will discuss the presence, formation, and role of myofibroblasts in SSc, and how these processes are stimulated and mediated by cells of the (innate) immune system such as mast cells and T helper 2 lymphocytes. Furthermore, current novel therapeutic approaches to target myofibroblasts will be highlighted for future perspective." @default.
- W2901760304 created "2018-11-29" @default.
- W2901760304 creator A5010536972 @default.
- W2901760304 creator A5040414977 @default.
- W2901760304 creator A5047159099 @default.
- W2901760304 creator A5057163360 @default.
- W2901760304 creator A5080344232 @default.
- W2901760304 date "2018-11-13" @default.
- W2901760304 modified "2023-10-01" @default.
- W2901760304 title "Unraveling SSc Pathophysiology; The Myofibroblast" @default.
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