Matches in SemOpenAlex for { <https://semopenalex.org/work/W2912258931> ?p ?o ?g. }
- W2912258931 endingPage "115" @default.
- W2912258931 startingPage "115" @default.
- W2912258931 abstract "The neuronal ceroid lipofuscinoses (NCLs) are a group of devastating neurological disorders that have a global distribution and affect people of all ages. Commonly known as Batten disease, this form of neurodegeneration is linked to mutations in 13 genetically distinct genes. The precise mechanisms underlying the disease are unknown, in large part due to our poor understanding of the functions of NCL proteins. The social amoeba Dictyostelium discoideum has proven to be an exceptional model organism for studying a wide range of neurological disorders, including the NCLs. The Dictyostelium genome contains homologs of 11 of the 13 NCL genes. Its life cycle, comprised of both single-cell and multicellular phases, provides an excellent system for studying the effects of NCL gene deficiency on conserved cellular and developmental processes. In this review, we highlight recent advances in NCL research using Dictyostelium as a biomedical model." @default.
- W2912258931 created "2019-02-21" @default.
- W2912258931 creator A5047772996 @default.
- W2912258931 creator A5087879282 @default.
- W2912258931 creator A5089578483 @default.
- W2912258931 date "2019-02-02" @default.
- W2912258931 modified "2023-10-07" @default.
- W2912258931 title "Recent Insights into NCL Protein Function Using the Model Organism Dictyostelium discoideum" @default.
- W2912258931 cites W107283145 @default.
- W2912258931 cites W1159100168 @default.
- W2912258931 cites W1536841578 @default.
- W2912258931 cites W1554964528 @default.
- W2912258931 cites W1863192597 @default.
- W2912258931 cites W186680452 @default.
- W2912258931 cites W1884093662 @default.
- W2912258931 cites W1962196811 @default.
- W2912258931 cites W1964864637 @default.
- W2912258931 cites W1965933552 @default.
- W2912258931 cites W1967660446 @default.
- W2912258931 cites W1972612511 @default.
- W2912258931 cites W1977845897 @default.
- W2912258931 cites W1984488513 @default.
- W2912258931 cites W1987117371 @default.
- W2912258931 cites W1988099826 @default.
- W2912258931 cites W1991870376 @default.
- W2912258931 cites W1996420041 @default.
- W2912258931 cites W1999643045 @default.
- W2912258931 cites W2002361420 @default.
- W2912258931 cites W2002982587 @default.
- W2912258931 cites W2005854095 @default.
- W2912258931 cites W2010865777 @default.
- W2912258931 cites W2020278806 @default.
- W2912258931 cites W2022909388 @default.
- W2912258931 cites W2023078387 @default.
- W2912258931 cites W2028721537 @default.
- W2912258931 cites W2035734706 @default.
- W2912258931 cites W2052160560 @default.
- W2912258931 cites W2055735666 @default.
- W2912258931 cites W2059030268 @default.
- W2912258931 cites W2061723574 @default.
- W2912258931 cites W2071054863 @default.
- W2912258931 cites W2073541618 @default.
- W2912258931 cites W2074308942 @default.
- W2912258931 cites W2074907621 @default.
- W2912258931 cites W2076488431 @default.
- W2912258931 cites W2080126760 @default.
- W2912258931 cites W2084394815 @default.
- W2912258931 cites W2084943702 @default.
- W2912258931 cites W2085963598 @default.
- W2912258931 cites W2088206463 @default.
- W2912258931 cites W2092217082 @default.
- W2912258931 cites W2096173332 @default.
- W2912258931 cites W2097741715 @default.
- W2912258931 cites W2098360662 @default.
- W2912258931 cites W2099726097 @default.
- W2912258931 cites W2112349449 @default.
- W2912258931 cites W2115679330 @default.
- W2912258931 cites W2119056118 @default.
- W2912258931 cites W2120814831 @default.
- W2912258931 cites W2127683402 @default.
- W2912258931 cites W2128339470 @default.
- W2912258931 cites W2128582098 @default.
- W2912258931 cites W2133788641 @default.
- W2912258931 cites W2138449564 @default.
- W2912258931 cites W2141531180 @default.
- W2912258931 cites W2145405617 @default.
- W2912258931 cites W2146715646 @default.
- W2912258931 cites W2148374260 @default.
- W2912258931 cites W2152480843 @default.
- W2912258931 cites W2155605495 @default.
- W2912258931 cites W2156850117 @default.
- W2912258931 cites W2157815460 @default.
- W2912258931 cites W2160126594 @default.
- W2912258931 cites W2160141505 @default.
- W2912258931 cites W2163300568 @default.
- W2912258931 cites W2163711162 @default.
- W2912258931 cites W2166574880 @default.
- W2912258931 cites W2169759563 @default.
- W2912258931 cites W2183718311 @default.
- W2912258931 cites W2288865678 @default.
- W2912258931 cites W2313201345 @default.
- W2912258931 cites W2315619403 @default.
- W2912258931 cites W2345764462 @default.
- W2912258931 cites W2527152174 @default.
- W2912258931 cites W2528717308 @default.
- W2912258931 cites W2551026518 @default.
- W2912258931 cites W2603532804 @default.
- W2912258931 cites W2605332501 @default.
- W2912258931 cites W2606376939 @default.
- W2912258931 cites W2610966021 @default.
- W2912258931 cites W2617688462 @default.
- W2912258931 cites W2619580074 @default.
- W2912258931 cites W272134036 @default.
- W2912258931 cites W2744220965 @default.
- W2912258931 cites W2765234120 @default.
- W2912258931 cites W2767619438 @default.
- W2912258931 cites W2768041729 @default.
- W2912258931 cites W2789908217 @default.