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- W2912694666 abstract "Periodic fever, aphthous stomatitis, pharyngitis, and cervical adenitis (PFAPA) syndrome is a complex autoinflammatory disease with a clinical phenotype characterised by recurrent episodes of fever, systemic inflammation and symptoms and signs depicted in disease acronym. Although PFAPA is the most common autoinflammatory disease among children in many parts of the world, the condition is still an enigma, which include the regular episodes, the prompt responses to corticosteroids, the genetic bases for the familial clustering and therapeutic effects of tonsillectomy. This review explores PFAPA syndrome with the aim of describing the current clinical and scientific understanding of the condition." @default.
- W2912694666 created "2019-02-21" @default.
- W2912694666 creator A5089843182 @default.
- W2912694666 date "2019-02-01" @default.
- W2912694666 modified "2023-10-01" @default.
- W2912694666 title "Periodic fever, aphthous stomatitis, pharyngitis, and cervical adenitis syndrome – PFAPA syndrome" @default.
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- W2912694666 doi "https://doi.org/10.1016/j.lpm.2018.08.016" @default.
- W2912694666 hasPubMedId "https://pubmed.ncbi.nlm.nih.gov/30683466" @default.
- W2912694666 hasPublicationYear "2019" @default.
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