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- W2913489911 endingPage "175" @default.
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- W2913489911 abstract "Pediatric pulmonary arterial hypertension (PAH) remains a rare and severe disease with a poor prognosis. PAH may be idiopathic, heritable or associated with systemic conditions in particular associated with congenital heart disease. Areas covered: A thorough and extensive diagnostic approach is required for a correct diagnosis. The outcome has improved over the last decade with a better diagnostic approach and with the initiation of new targeted therapies. However, there is still significant progress to achieve as there is still no cure for this devastating disease. Expert opinion: Adapted clinical studies to define the best therapeutic approach are needed. Even if the treatment approach is still mainly derived from adult data and expert consensus, several studies and registries are currently underway and should deliver important information in the next future. This review aims to give an overview of the current diagnosis and treatment strategies of PAH." @default.
- W2913489911 created "2019-02-21" @default.
- W2913489911 creator A5004729513 @default.
- W2913489911 creator A5008018023 @default.
- W2913489911 creator A5049472882 @default.
- W2913489911 date "2019-02-12" @default.
- W2913489911 modified "2023-09-24" @default.
- W2913489911 title "Diagnosis and treatment of pediatric pulmonary arterial hypertension" @default.
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- W2913489911 doi "https://doi.org/10.1080/14779072.2019.1576523" @default.
- W2913489911 hasPubMedId "https://pubmed.ncbi.nlm.nih.gov/30698043" @default.
- W2913489911 hasPublicationYear "2019" @default.