Matches in SemOpenAlex for { <https://semopenalex.org/work/W2922513760> ?p ?o ?g. }
- W2922513760 abstract "A proportion of patients with certain types of interstitial lung disease (ILD), including chronic hypersensitivity pneumonitis and ILDs associated with autoimmune diseases, develop a progressive fibrosing phenotype that shows similarities in clinical course to idiopathic pulmonary fibrosis. Irrespective of the clinical diagnosis, these progressive fibrosing ILDs show commonalities in the underlying pathogenetic mechanisms that drive a self-sustaining process of pulmonary fibrosis. The natural history of progressive fibrosing ILDs is characterized by decline in lung function, worsening of symptoms and health-related quality of life, and early mortality. Greater impairment in forced vital capacity or diffusion capacity of the lungs for carbon monoxide, and a greater extent of fibrotic changes on a computed tomography scan, are predictors of mortality in patients with fibrosing ILDs. However, the course of these diseases is heterogenous and cannot accurately be predicted for an individual patient. Data from ongoing clinical trials and patient registries will provide a better understanding of the clinical course and impact of progressive fibrosing ILDs." @default.
- W2922513760 created "2019-03-22" @default.
- W2922513760 creator A5011774869 @default.
- W2922513760 creator A5061112564 @default.
- W2922513760 date "2019-03-14" @default.
- W2922513760 modified "2023-10-16" @default.
- W2922513760 title "The natural history of progressive fibrosing interstitial lung diseases" @default.
- W2922513760 cites W1531708583 @default.
- W2922513760 cites W1651567174 @default.
- W2922513760 cites W1857071204 @default.
- W2922513760 cites W1858708506 @default.
- W2922513760 cites W1885525613 @default.
- W2922513760 cites W1924766221 @default.
- W2922513760 cites W1954728404 @default.
- W2922513760 cites W1998471540 @default.
- W2922513760 cites W1999439792 @default.
- W2922513760 cites W2002587076 @default.
- W2922513760 cites W2007414618 @default.
- W2922513760 cites W2017258499 @default.
- W2922513760 cites W2022441502 @default.
- W2922513760 cites W2031123734 @default.
- W2922513760 cites W2037645843 @default.
- W2922513760 cites W2042096696 @default.
- W2922513760 cites W2056932041 @default.
- W2922513760 cites W2058234974 @default.
- W2922513760 cites W2063946490 @default.
- W2922513760 cites W2067439241 @default.
- W2922513760 cites W2078317932 @default.
- W2922513760 cites W2093907019 @default.
- W2922513760 cites W2095657111 @default.
- W2922513760 cites W2096879602 @default.
- W2922513760 cites W2098530232 @default.
- W2922513760 cites W2102305559 @default.
- W2922513760 cites W2107665433 @default.
- W2922513760 cites W2108406461 @default.
- W2922513760 cites W2110777286 @default.
- W2922513760 cites W2113582838 @default.
- W2922513760 cites W2115503161 @default.
- W2922513760 cites W2116521677 @default.
- W2922513760 cites W2116531828 @default.
- W2922513760 cites W2116971462 @default.
- W2922513760 cites W2120480075 @default.
- W2922513760 cites W2120504173 @default.
- W2922513760 cites W2122497863 @default.
- W2922513760 cites W2125013258 @default.
- W2922513760 cites W2130052733 @default.
- W2922513760 cites W2131014787 @default.
- W2922513760 cites W2143551777 @default.
- W2922513760 cites W2144111246 @default.
- W2922513760 cites W2145323940 @default.
- W2922513760 cites W2146484111 @default.
- W2922513760 cites W2146945647 @default.
- W2922513760 cites W2157572334 @default.
- W2922513760 cites W2160262606 @default.
- W2922513760 cites W2160639837 @default.
- W2922513760 cites W2164738490 @default.
- W2922513760 cites W2169645723 @default.
- W2922513760 cites W2172237567 @default.
- W2922513760 cites W2179863481 @default.
- W2922513760 cites W2197347269 @default.
- W2922513760 cites W2198090250 @default.
- W2922513760 cites W2260133387 @default.
- W2922513760 cites W2270214041 @default.
- W2922513760 cites W2340054689 @default.
- W2922513760 cites W2440054067 @default.
- W2922513760 cites W2468480403 @default.
- W2922513760 cites W2486571869 @default.
- W2922513760 cites W2513267980 @default.
- W2922513760 cites W2544634021 @default.
- W2922513760 cites W2547041957 @default.
- W2922513760 cites W2550171723 @default.
- W2922513760 cites W2551533543 @default.
- W2922513760 cites W2590518859 @default.
- W2922513760 cites W2591396264 @default.
- W2922513760 cites W2592669695 @default.
- W2922513760 cites W2603140425 @default.
- W2922513760 cites W2604367936 @default.
- W2922513760 cites W2605548119 @default.
- W2922513760 cites W2605649105 @default.
- W2922513760 cites W2613282762 @default.
- W2922513760 cites W2623730400 @default.
- W2922513760 cites W2624827840 @default.
- W2922513760 cites W2625915911 @default.
- W2922513760 cites W2626574050 @default.
- W2922513760 cites W2654481826 @default.
- W2922513760 cites W2734975932 @default.
- W2922513760 cites W2750520295 @default.
- W2922513760 cites W2750715393 @default.
- W2922513760 cites W2751340690 @default.
- W2922513760 cites W2755069867 @default.
- W2922513760 cites W2756466752 @default.
- W2922513760 cites W2760207887 @default.
- W2922513760 cites W2765883004 @default.
- W2922513760 cites W2770778260 @default.
- W2922513760 cites W2775612423 @default.
- W2922513760 cites W2784006802 @default.
- W2922513760 cites W2791389722 @default.
- W2922513760 cites W2797176335 @default.
- W2922513760 cites W2799479598 @default.
- W2922513760 cites W2803162668 @default.