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- W2927053191 abstract "Recurrent acute and chronic lung infections associated with bronchiectasis are a major cause of morbidity and mortality in patients with primary immunodeficiency disorders (PIDs).1-3 In adults, inflammatory interstitial lung disease (ILD) not due to pyogenic infection is found in up to 20% of patients with common variable immunodeficiency disorders (CVID) and can be associated with progressive restrictive lung disease and shortened survival.4,5 High-resolution chest computed tomography (CT) scan is the gold standard imaging technique for diagnosing ILD." @default.
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- W2927053191 date "2019-09-01" @default.
- W2927053191 modified "2023-10-16" @default.
- W2927053191 title "Life-threatening pulmonary interstitial lung disease complicating pediatric nonhumoral immunodeficiencies" @default.
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- W2927053191 doi "https://doi.org/10.1016/j.jaip.2019.03.034" @default.
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