Matches in SemOpenAlex for { <https://semopenalex.org/work/W2955985773> ?p ?o ?g. }
- W2955985773 abstract "Abstract Malformation syndromes with predisposition to peripheral neuroblastic tumors (pNT), including neuroblastoma, ganglioneuroblastoma, and ganglioneuroma, may provide clues to critical mutations influencing pNT development. Our objective was to identify and characterize features of pNT associated with specific malformation syndromes. A systematic review of the literature was performed using MEDLINE, Scopus, and Web of Science. We identified 154 of 1014 papers that met eligibility, comprising 207 cases. The patient's age, tumor histology, and frequency of multiple primary tumors varied by malformation syndrome. Genomic studies and systematized reporting are necessary to elucidate cancer risk and the distinct clinical and biological pNT patterns within syndromes." @default.
- W2955985773 created "2019-07-12" @default.
- W2955985773 creator A5017840054 @default.
- W2955985773 creator A5077444414 @default.
- W2955985773 creator A5080600507 @default.
- W2955985773 date "2019-07-02" @default.
- W2955985773 modified "2023-10-16" @default.
- W2955985773 title "Congenital malformation syndromes associated with peripheral neuroblastic tumors: A systematic review" @default.
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