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- W3015133089 abstract "Hypertriglyceridemia (HTG) can result from a variety of causes. Mild to moderate HTG occurs commonly as part of the metabolic syndrome, can be the result of multiple genetic mutations in an individual or family, and can be secondary to several diseases and drugs. Severe HTG with plasma triglyceride (TG) levels >1000-1500 mg/dL can result from 3 groups of conditions: (1) rare mutations in the lipoprotein lipase (LPL) complex, where it is termed the familial chylomicronemia syndrome (FCS), (2) the co-existence of genetic and secondary forms of HTG, termed the multifactorial chylomicronemia syndrome (MFCS), which is a much more common cause of severe HTG, and (3) familial partial lipodystrophy (FPLD). Mild to moderate HTG is associated with an increased risk of premature cardiovascular disease (CVD), while severe HTG can lead to pancreatitis and other features of the chylomicronemia syndrome, as well as an increased risk of premature CVD. Appropriate management of the patient with HTG requires knowledge of the likely cause of the HTG, in order to prevent its complications. For complete coverage of all related areas of Endocrinology, please visit our on-line FREE web-text, WWW.ENDOTEXT.ORG ." @default.
- W3015133089 created "2020-04-10" @default.
- W3015133089 creator A5022745436 @default.
- W3015133089 creator A5062614749 @default.
- W3015133089 date "2000-01-01" @default.
- W3015133089 modified "2023-09-27" @default.
- W3015133089 title "Hypertriglyceridemia: Pathophysiology, Role of Genetics, Consequences, and Treatment" @default.
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