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- W3017003623 abstract "El síndrome de Herlyn-Werner-Wunderlich (HWW) es una anomalía congénita rara que consiste en una hemivagina obstruida en útero didelfo asociado, en numerosas ocasiones, a agénesis renal ipsolateral. Se presenta un caso de una paciente de 31 años, sin antecedentes médicos importantes, con metrorragia escasa, intermitente y maloliente de 2-3 meses de evolución. En la exploración vaginal intraoperatoria se visualizaron un cérvix hipotrófico y un orificio externo de un trayecto fistuloso que comunicaba con la cavidad uterina derecha y drenaba material hemático oscuro. La urografía intravenosa constató una agenesia renal derecha y confirmó el diagnóstico. Uterus didelphys with obstructed hemivagina frequently associated with ipsilateral renal agenesis is a rare congenital anomaly known as Herlyn-Werner-Wunderlich syndrome (HWW). We report the case of a 31-year-old woman with no relevant medical history, with scant, intermittent and ill-smelling metrorrhagia for the last 2-3 months. Intraoperative vaginal exploration revealed a hypotrophic cervix and the external orifice of a fistula communicating with the right uterine cavity and draining a dark hematic fluid. Intravenous urography showed right renal agenesis and confirmed the suspected diagnosis of HWW." @default.
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- W3017003623 date "2012-10-01" @default.
- W3017003623 modified "2023-09-27" @default.
- W3017003623 title "Síndrome de Herlyn-Werner-Wunderlich" @default.
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- W3017003623 doi "https://doi.org/10.1016/j.pog.2011.06.017" @default.
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