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- W3021216556 abstract "淋巴管平滑肌瘤病(LAM)是一种少见的系统性低度恶性肿瘤性疾病。LAM合并乳糜肺炎较为少见,易误诊、漏诊。本文报道1例LAM合并乳糜肺炎,患者胸部CT示双肺散在小圆形囊状透亮影、斑片影、磨玻璃影。血清血管内皮生长因子D(VEGF-D)11 370.2 ng/L,痰乳糜试验阳性。腹部CT示腹膜后可见多发低密度团块影。予西罗莫司维持治疗(血药浓度5~10 μg/L),随访18个月,患者症状改善,肺部病变、腹部病变逐渐吸收,血清VEGF-D水平降至3 231.9 ng/L。胸部CT示肺部出现小叶间隔增厚,磨玻璃影、斑片影等影像学表现时,需考虑乳糜肺炎可能;VEGF-D对该病的诊断和疗效评估具有重要意义;西罗莫司对LAM合并乳糜肺炎疗效显著,但其长期使用的有效性、安全性需进一步探究。." @default.
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- W3021216556 date "2020-05-01" @default.
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- W3021216556 title "[A case of lymphangiomyomatosis accompanied with chylous pneumonia]." @default.
- W3021216556 doi "https://doi.org/10.3760/cma.j.cn112138-20200226-00134" @default.
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