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- W3025786733 endingPage "22" @default.
- W3025786733 startingPage "1" @default.
- W3025786733 abstract "Amyotrophic lateral sclerosis is an adult onset, fatal neurodegenerative disorder, involving the large motor neurons of the brain and the spinal cord. It is characterized clinically by progressive paralysis and eventual death from respiratory failure in three to five years. Although ALS is mainly a sporadic disease, about 10% of ALS cases are familial. To date at least 10 genes have been identified that cause familial ALS with SOD1 being the first to be discovered. These genes have allowed animal modeling of familial ALS, which has been instrumental in understanding disease pathogenesis and in testing different therapies. More recently, the tools of modern genetics have also been applied to sporadic ALS in an attempt to decipher the complex genetic and environmental interactions that cause this fatal disease." @default.
- W3025786733 created "2020-05-21" @default.
- W3025786733 creator A5011023696 @default.
- W3025786733 creator A5061347020 @default.
- W3025786733 creator A5063753709 @default.
- W3025786733 date "2013-01-01" @default.
- W3025786733 modified "2023-10-14" @default.
- W3025786733 title "Motor Neuron Disease" @default.
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