Matches in SemOpenAlex for { <https://semopenalex.org/work/W3041476349> ?p ?o ?g. }
- W3041476349 endingPage "1851" @default.
- W3041476349 startingPage "1851" @default.
- W3041476349 abstract "Desmoid tumors represent a rare entity of monoclonal origin characterized by locally aggressive behavior and inability to metastasize. Most cases present in a sporadic pattern and are characterized by a mutation in the CTNNB1 gene; while 5–15% show a hereditary pattern associated with APC gene mutation, both resulting in abnormal β-catenin accumulation within the cell. The most common sites of presentation are the extremities and the thoracic wall, whereas FAP associated cases present intra-abdominally or in the abdominal wall. Histopathological diagnosis is mandatory, and evaluation is guided with imaging studies ranging from ultrasound, computed tomography or magnetic resonance. Current approaches advocate for an initial active surveillance period due to the stabilization and even regression capacity of desmoid tumors. For progressive, symptomatic, or disabling cases, systemic treatment, radiotherapy or surgery may be used. This is a narrative review of this uncommon disease; we present current knowledge about molecular pathogenesis, diagnosis and treatment." @default.
- W3041476349 created "2020-07-16" @default.
- W3041476349 creator A5016167599 @default.
- W3041476349 creator A5020419421 @default.
- W3041476349 creator A5061353536 @default.
- W3041476349 creator A5065283758 @default.
- W3041476349 creator A5075539937 @default.
- W3041476349 creator A5085059186 @default.
- W3041476349 creator A5085655796 @default.
- W3041476349 creator A5090176879 @default.
- W3041476349 date "2020-07-09" @default.
- W3041476349 modified "2023-10-14" @default.
- W3041476349 title "Desmoid-Type Fibromatosis" @default.
- W3041476349 cites W1564324635 @default.
- W3041476349 cites W1798211820 @default.
- W3041476349 cites W1910192533 @default.
- W3041476349 cites W1967653001 @default.
- W3041476349 cites W1970852339 @default.
- W3041476349 cites W1977172662 @default.
- W3041476349 cites W1985117013 @default.
- W3041476349 cites W1987495766 @default.
- W3041476349 cites W1993867849 @default.
- W3041476349 cites W2001315495 @default.
- W3041476349 cites W2003852692 @default.
- W3041476349 cites W2012130219 @default.
- W3041476349 cites W2019686527 @default.
- W3041476349 cites W2034815219 @default.
- W3041476349 cites W2038302582 @default.
- W3041476349 cites W2043751048 @default.
- W3041476349 cites W2045479207 @default.
- W3041476349 cites W2046792469 @default.
- W3041476349 cites W2049718819 @default.
- W3041476349 cites W2050858148 @default.
- W3041476349 cites W2053453318 @default.
- W3041476349 cites W2054012674 @default.
- W3041476349 cites W2054080205 @default.
- W3041476349 cites W2059674083 @default.
- W3041476349 cites W2070605120 @default.
- W3041476349 cites W2071497196 @default.
- W3041476349 cites W2073052893 @default.
- W3041476349 cites W2094141932 @default.
- W3041476349 cites W2095459863 @default.
- W3041476349 cites W2099147205 @default.
- W3041476349 cites W2106365164 @default.
- W3041476349 cites W2116318030 @default.
- W3041476349 cites W2116970128 @default.
- W3041476349 cites W2119274552 @default.
- W3041476349 cites W2120353499 @default.
- W3041476349 cites W2124819146 @default.
- W3041476349 cites W2135312069 @default.
- W3041476349 cites W2141205256 @default.
- W3041476349 cites W2143458022 @default.
- W3041476349 cites W2150583786 @default.
- W3041476349 cites W2151879946 @default.
- W3041476349 cites W2152015156 @default.
- W3041476349 cites W2181787708 @default.
- W3041476349 cites W2258278932 @default.
- W3041476349 cites W2296375360 @default.
- W3041476349 cites W2326804101 @default.
- W3041476349 cites W2409457994 @default.
- W3041476349 cites W2479605255 @default.
- W3041476349 cites W2517285723 @default.
- W3041476349 cites W2560667500 @default.
- W3041476349 cites W2588964575 @default.
- W3041476349 cites W2610129321 @default.
- W3041476349 cites W2613792049 @default.
- W3041476349 cites W2618835482 @default.
- W3041476349 cites W2620740560 @default.
- W3041476349 cites W2669144980 @default.
- W3041476349 cites W2751153944 @default.
- W3041476349 cites W2771505163 @default.
- W3041476349 cites W2883672481 @default.
- W3041476349 cites W2888865283 @default.
- W3041476349 cites W2900605163 @default.
- W3041476349 cites W2905567470 @default.
- W3041476349 cites W2963740442 @default.
- W3041476349 cites W2974418538 @default.
- W3041476349 cites W3004209283 @default.
- W3041476349 cites W3008368007 @default.
- W3041476349 cites W3019390237 @default.
- W3041476349 cites W4290302474 @default.
- W3041476349 cites W4295682055 @default.
- W3041476349 cites W73782554 @default.
- W3041476349 cites W92944290 @default.
- W3041476349 doi "https://doi.org/10.3390/cancers12071851" @default.
- W3041476349 hasPubMedCentralId "https://www.ncbi.nlm.nih.gov/pmc/articles/7408653" @default.
- W3041476349 hasPubMedId "https://pubmed.ncbi.nlm.nih.gov/32660036" @default.
- W3041476349 hasPublicationYear "2020" @default.
- W3041476349 type Work @default.
- W3041476349 sameAs 3041476349 @default.
- W3041476349 citedByCount "36" @default.
- W3041476349 countsByYear W30414763492021 @default.
- W3041476349 countsByYear W30414763492022 @default.
- W3041476349 countsByYear W30414763492023 @default.
- W3041476349 crossrefType "journal-article" @default.
- W3041476349 hasAuthorship W3041476349A5016167599 @default.
- W3041476349 hasAuthorship W3041476349A5020419421 @default.
- W3041476349 hasAuthorship W3041476349A5061353536 @default.