Matches in SemOpenAlex for { <https://semopenalex.org/work/W3096752746> ?p ?o ?g. }
Showing items 1 to 54 of
54
with 100 items per page.
- W3096752746 abstract "Pulmonary alveolar microlithiasis (PAM) is a rare autosomal recessive lung disease. It is characterized by the accumulation of calculi called microliths. There is no definitive treatment. Disodium etidronate has been administered due to its alleged calcium phosphate precipitation-reducing effect; however, its effectiveness is controversial. Case; A 13-year-old male referred because of the reticulonodular opacities in chest X-ray detected during evaluation for upper respiratory tract infection. Pulmonary function test results showed a mild restrictive pattern. Findings on computed tomographic (CT) images were consistent with interstitial lung disease. Open lung biopsy confirmed a diagnosis of PAM. The patient started disodium etidronate treatment. Sandstorm-like appearance on chest x-ray decrease and restrictive pattern in pulmonary function test improved after six months of treatment. There was no significant change in CT. After cessation of treatment, the patient remains stable clinically. His asymptomatic sister also screened and similar mutation in SLC34A2 detected. However, because of his sister asymptomatic and younger, she is followed without treatment and remained stable clinically. Conclusion: Currently, there is no consensus on the treatment of PAM. The number of the report describes the beneficial effects of long-term treatment with disodium etidronate, but in a certain case, it seems ineffective. Our patient9s chest X-ray and pulmonary function improved after six months of disodium etidronate treatment. However, there was no major change in CT. He remains asymptomatic after discontinuation of treatment. Therefore, the effectiveness of disodium etidronate still remains controversial." @default.
- W3096752746 created "2020-11-09" @default.
- W3096752746 creator A5019299964 @default.
- W3096752746 creator A5021905831 @default.
- W3096752746 creator A5031783306 @default.
- W3096752746 creator A5052203721 @default.
- W3096752746 creator A5074074792 @default.
- W3096752746 date "2020-09-07" @default.
- W3096752746 modified "2023-09-22" @default.
- W3096752746 title "Effect of Disodium Etidronate in Patient With Pulmonary Alveolar Microlithiasis" @default.
- W3096752746 doi "https://doi.org/10.1183/13993003.congress-2020.3491" @default.
- W3096752746 hasPublicationYear "2020" @default.
- W3096752746 type Work @default.
- W3096752746 sameAs 3096752746 @default.
- W3096752746 citedByCount "0" @default.
- W3096752746 crossrefType "proceedings-article" @default.
- W3096752746 hasAuthorship W3096752746A5019299964 @default.
- W3096752746 hasAuthorship W3096752746A5021905831 @default.
- W3096752746 hasAuthorship W3096752746A5031783306 @default.
- W3096752746 hasAuthorship W3096752746A5052203721 @default.
- W3096752746 hasAuthorship W3096752746A5074074792 @default.
- W3096752746 hasConcept C126322002 @default.
- W3096752746 hasConcept C141071460 @default.
- W3096752746 hasConcept C2777543607 @default.
- W3096752746 hasConcept C2777714996 @default.
- W3096752746 hasConcept C2777910003 @default.
- W3096752746 hasConcept C2778715236 @default.
- W3096752746 hasConcept C71924100 @default.
- W3096752746 hasConcept C75603125 @default.
- W3096752746 hasConceptScore W3096752746C126322002 @default.
- W3096752746 hasConceptScore W3096752746C141071460 @default.
- W3096752746 hasConceptScore W3096752746C2777543607 @default.
- W3096752746 hasConceptScore W3096752746C2777714996 @default.
- W3096752746 hasConceptScore W3096752746C2777910003 @default.
- W3096752746 hasConceptScore W3096752746C2778715236 @default.
- W3096752746 hasConceptScore W3096752746C71924100 @default.
- W3096752746 hasConceptScore W3096752746C75603125 @default.
- W3096752746 hasLocation W30967527461 @default.
- W3096752746 hasOpenAccess W3096752746 @default.
- W3096752746 hasPrimaryLocation W30967527461 @default.
- W3096752746 hasRelatedWork W10944005 @default.
- W3096752746 hasRelatedWork W1402687 @default.
- W3096752746 hasRelatedWork W15963216 @default.
- W3096752746 hasRelatedWork W2017735 @default.
- W3096752746 hasRelatedWork W20592763 @default.
- W3096752746 hasRelatedWork W2677851 @default.
- W3096752746 hasRelatedWork W4407459 @default.
- W3096752746 hasRelatedWork W5404319 @default.
- W3096752746 hasRelatedWork W8391396 @default.
- W3096752746 hasRelatedWork W938291 @default.
- W3096752746 isParatext "false" @default.
- W3096752746 isRetracted "false" @default.
- W3096752746 magId "3096752746" @default.
- W3096752746 workType "article" @default.