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- W3113662394 endingPage "16" @default.
- W3113662394 startingPage "9" @default.
- W3113662394 abstract "Cystic fibrosis (CF) - although primarily a lung disease - also causes a variety of gastrointestinal manifestations which are important for diagnosis, prognosis and quality of life. All parts of the gastrointestinal tract can be affected by CF. Besides the well-known pancreatic insufficiency, gastroesophageal reflux disease, liver disease and diseases of the large intestine are important pathologies that impact on prognosis and also impair quality of life. Diagnosis and management of gastrointestinal manifestations will be discussed in this review. Since optimisation of CF therapy is associated with a significantly longer life-span of CF patients nowadays, also gastrointestinal malignancies, which are more common in CF than in the non-CF population need to be considered. Furthermore, novel evidence on the role of the gut microbiome in CF is emerging. The introduction of cystic fibrosis transmembrane conductance regulator (CFTR) protein modulators gives hope for symptom alleviation and even cure of gastrointestinal manifestations of CF." @default.
- W3113662394 created "2021-01-05" @default.
- W3113662394 creator A5014193257 @default.
- W3113662394 creator A5016028088 @default.
- W3113662394 creator A5029730706 @default.
- W3113662394 date "2022-06-01" @default.
- W3113662394 modified "2023-10-18" @default.
- W3113662394 title "Changing paradigms in the treatment of gastrointestinal complications of cystic fibrosis in the era of cystic fibrosis transmembrane conductance regulator modulators" @default.
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