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- W3136602801 abstract "47歳女性.1か月半で四肢の筋痛,筋力低下,嚥下障害が進行し,MRIで四肢近位筋・体幹筋に炎症を示唆する異常信号域を認めたが,入院時に皮膚所見はみられなかった.左上腕二頭筋の筋生検では筋束周囲性萎縮(perifascicular atrophy)の所見はなかったが,筋線維でのmyxovirus resistance protein A発現と血清抗nuclear matrix protein(NXP)-2抗体陽性から皮膚筋炎(dermatomyositis,以下DMと略記)と確定診断した.副腎皮質ステロイド,免疫抑制剤,免疫グロブリン療法で症状は徐々に改善した.皮膚所見がないDMもあることを念頭に,抗NXP-2抗体を含む筋炎特異的自己抗体の測定を積極的に検討すべきと考えられる." @default.
- W3136602801 created "2021-03-29" @default.
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- W3136602801 date "2021-01-01" @default.
- W3136602801 modified "2023-10-16" @default.
- W3136602801 title "A case of dermatomyositis positive for anti-nuclear matrix protein 2 antibody without dermatologic symptoms" @default.
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- W3136602801 doi "https://doi.org/10.5692/clinicalneurol.cn-001528" @default.
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