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- W3150205611 abstract "RESUME But. Determiner la prevalence de la retinopathie drepanocytaire dans une population de drepanocytaires homozygotes SS. Patients et methodes. Lors de la celebration de la journee mondiale de la drepanocytose en 2016, les patients drepanocytaires SS connus ayant donne leur consentement ont ete inclus dans une etude transversale et descriptive qui s’est deroulee du 13 au 17 juin 2016. L’examen ophtalmologique comprenait : la mesure de l’acuite visuelle et de la pression intraoculaire ; l’examen du segment anterieur a la lampe a fente et le fond œil avec un verre a trois miroirs. Le verre a trois miroirs n’a pas ete pose chez les enfants de moins de 5 ans. L’angiographie a la fluoresceine a ete realisee lorsque le patient presentait des signes d’ischemie retinienne peripherique. La classification de Goldberg a ete utilisee pour la retinopathie. Resultats. Quatre-vingt-huit patients ont ete inclus, dont 49 (55,7%) etaient de sexe feminin et 39 (44,3%) de sexe masculin. L’âge moyen des patients etait de 12,6 ± 9,7 ans avec les extremes de 3 ans et 47 ans. L’examen au verre a trois miroirs a ete realise chez 81 patients (≥ 5 ans). Il etait normal dans 52,5% des yeux (n=85 /162). La retinopathie etait presente dans 36 yeux (n=36/162 ; 22,2%). Elle etait non-proliferante dans 35 yeux (n=35/162 ; 21,6%) et proliferante dans un œil (0,6%). Les autres anomalies notees etaient : la tortuosite veineuse (n=37 ; 22,8%) ; les mottes pigmentaires (n=3 ; 1,9%) et la pâleur papillaire (n=2 ; 1,2%). Conclusion. La retinopathie drepanocytaire proliferante bien que rare chez les drepanocytaires homozygotes SS, merite un depistage car ses complications sont cecitantes.ABSTRACTAim. To determine the prevalence of sickle cell retinopathy in a population of homozygous sickle cell patients. Patients and methods. On the celebration of the world sickle cell day in 2016, consenting known homozygous SS patients were included in a cross-sectional, descriptive study which spanned 13th to 17th June 2016. Ophthalmic examination included the measurement of visual acuity and intraocular pressure; slit lamp anterior segment examination and three-mirror lens examination of the fundus. Fluorescein angiography was done in the presence of peripheral retinal ischemia. Goldberg’s classification of sickle cell retinopathy was used. Results. Eighty-eight patients were included, amongst whom 49 (55.7%) females and 39 (44.3%) males. The mean age was 12.6 ± 9.7 years, with extremes of 3 and 47 years. Three-mirror lens examination was done in 81 patients. It was normal in 52.5% of eyes (n=85 /162). Retinopathy was present in 36 eyes (22.2%). It was non-proliferative in 35 eyes (21.6%) and proliferative in one eye (0.6%). Other abnormal findings included venous tortuosity (n=37; 22.8%); pigment degeneration (n=3; 1.9%) and disc pallor (n=2; 1.2%). Conclusion. proliferative sickle cell retinopathy in rare amongst homozygote SS patients however, screening is important because of its blinding complications." @default.
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- W3150205611 date "2021-03-28" @default.
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- W3150205611 title "Prévalence de la Rétinopathie Drépanocytaire chez les Homozygotes SS à Yaoundé" @default.
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