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- W3151845020 endingPage "117425" @default.
- W3151845020 startingPage "117425" @default.
- W3151845020 abstract "Inflammatory cerebral amyloid angiopathy is a largely reversible inflammatory vasculopathy that develops in an acute or subacute fashion in reaction to amyloid protein deposition in the central nervous system blood vessels. There are two recognized pathologically characterized variants: cerebral amyloid angiopathy-related inflammation (CAAri) and A beta-related angiitis (ABRA). Both variants produce a clinical picture that resembles primary angiitis of the CNS but is distinguished by a characteristic radiologic appearance. Although originally defined as a clinicopathologic diagnosis, it can now often be diagnosed based on clinicoradiologic criteria, though confirmation with brain and meningeal biopsy is still required in some cases. This disorder typically responds to steroids but addition of other immune suppressants may be needed in some cases to control the disease." @default.
- W3151845020 created "2021-04-13" @default.
- W3151845020 creator A5028305623 @default.
- W3151845020 date "2021-05-01" @default.
- W3151845020 modified "2023-10-15" @default.
- W3151845020 title "Cerebral amyloid angiopathy and related inflammatory disorders" @default.
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