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- W3152146516 abstract "门静脉(CAPV ) 的先天的缺席是在过去的一个稀罕事件。然而,因为进展,检测 CAPV 案例的数字在成像技术在最近的年里增加了。有与门静脉高血压(PH ) 或 portosystemic 脑病(PSE ) 在场的 CAPV 的病人,而是这些条件很少发生直到病人长大或变得旧。病人通常为静脉的分流, ultrasonography (美国) 检测的肝或心脏的畸形,计算断层摄影术(CT ) 和磁性的回声成像(MRI ) 的复杂并发症访问医生。这疾病的病原学不是清楚的,但是大多数调查者认为它与门静脉的反常胚胎学的开发被联系。通常,外科的干预能减轻症状并且在 CAPV 病人阻止复杂并发症的出现。而且,它的管理应该在一个个别基础上被强调,取决于疾病,以及症状和病人的临床的条件的类型或解剖。" @default.
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- W3152146516 date "2008-01-01" @default.
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- W3152146516 title "Insight into congenital absence of the portal vein: Is it rare?" @default.
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