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- W3154804842 endingPage "3827" @default.
- W3154804842 startingPage "3827" @default.
- W3154804842 abstract "Mammalian mitochondrial ribosomes (mitoribosomes) synthesize a small subset of proteins, which are essential components of the oxidative phosphorylation machinery. Therefore, their function is of fundamental importance to cellular metabolism. The assembly of mitoribosomes is a complex process that progresses through numerous maturation and protein-binding events coordinated by the actions of several assembly factors. Dysregulation of mitoribosome production is increasingly recognized as a contributor to metabolic and neurodegenerative diseases. In recent years, mutations in multiple components of the mitoribosome assembly machinery have been associated with a range of human pathologies, highlighting their importance to cell function and health. Here, we provide a review of our current understanding of mitoribosome biogenesis, highlighting the key factors involved in this process and the growing number of mutations in genes encoding mitoribosomal RNAs, proteins, and assembly factors that lead to human disease." @default.
- W3154804842 created "2021-04-26" @default.
- W3154804842 creator A5004411213 @default.
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- W3154804842 creator A5037949533 @default.
- W3154804842 creator A5038824820 @default.
- W3154804842 creator A5066457081 @default.
- W3154804842 date "2021-04-07" @default.
- W3154804842 modified "2023-10-15" @default.
- W3154804842 title "Human Mitoribosome Biogenesis and Its Emerging Links to Disease" @default.
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