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- W3204309866 endingPage "71" @default.
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- W3204309866 abstract "Abstract Cardiolipin (CL) is the signature phospholipid (PL) of mitochondria and plays a pivotal role in mitochondrial and cellular function. Disruption of the CL remodeling gene tafazzin ( TAZ ) causes the severe genetic disorder Barth syndrome (BTHS). Our current understanding of the function of CL and the mechanism underlying the disease has greatly benefited from studies utilizing the powerful yeast model Saccharomyces cerevisiae . In this review, we discuss important findings on the function of CL and its remodeling from yeast studies and the implications of these findings for BTHS, highlighting the potential physiological modifiers that may contribute to the disparities in clinical presentation among BTHS patients." @default.
- W3204309866 created "2021-10-11" @default.
- W3204309866 creator A5013405117 @default.
- W3204309866 creator A5064512740 @default.
- W3204309866 date "2021-10-19" @default.
- W3204309866 modified "2023-10-16" @default.
- W3204309866 title "Cardiolipin function in the yeast <i>S. cerevisiae</i> and the lessons learned for Barth syndrome" @default.
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