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- W3204961664 endingPage "608" @default.
- W3204961664 startingPage "577" @default.
- W3204961664 abstract "Abstract Primary cilia are dynamic compartments that regulate multiple aspects of cellular signaling. The production, maintenance, and function of cilia involve more than 1000 genes in mammals, and their mutations disrupt the ciliary signaling which manifests in a plethora of pathological conditions—the ciliopathies. Skeletal ciliopathies are genetic disorders affecting the development and homeostasis of the skeleton, and encompass a broad spectrum of pathologies ranging from isolated polydactyly to lethal syndromic dysplasias. The recent advances in forward genetics allowed for the identification of novel regulators of skeletogenesis, and revealed a growing list of ciliary proteins that are critical for signaling pathways implicated in bone physiology. Among these, a group of protein kinases involved in cilia assembly, maintenance, signaling, and disassembly has emerged. In this review, we summarize the functions of cilia kinases in skeletal development and disease, and discuss the available and upcoming treatment options." @default.
- W3204961664 created "2021-10-11" @default.
- W3204961664 creator A5002837748 @default.
- W3204961664 creator A5026718940 @default.
- W3204961664 creator A5029793866 @default.
- W3204961664 creator A5034002466 @default.
- W3204961664 date "2021-10-18" @default.
- W3204961664 modified "2023-10-04" @default.
- W3204961664 title "Cilia kinases in skeletal development and homeostasis" @default.
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