Matches in SemOpenAlex for { <https://semopenalex.org/work/W3207712170> ?p ?o ?g. }
- W3207712170 endingPage "483" @default.
- W3207712170 startingPage "471" @default.
- W3207712170 abstract "As brutally demonstrated by the COVID-19 pandemic, an effective immune system is essential for survival. Developed over evolutionary time, viral nucleic acid detection is a central pillar in the defensive armamentarium used to combat foreign microbial invasion. To ensure cellular homeostasis, such a strategy necessitates the efficient discrimination of pathogen-derived DNA and RNA from that of the host. In 2011, it was suggested that an upregulation of type I interferon signalling might serve as a defining feature of a novel set of Mendelian inborn errors of immunity, where antiviral sensors are triggered by host nucleic acids due to a failure of self versus non-self discrimination. These rare disorders have played a surprisingly significant role in informing our understanding of innate immunity and the relevance of type I interferon signalling for human health and disease. Here we consider what we have learned in this time, and how the field may develop in the future." @default.
- W3207712170 created "2021-10-25" @default.
- W3207712170 creator A5013758087 @default.
- W3207712170 creator A5053471909 @default.
- W3207712170 date "2021-10-20" @default.
- W3207712170 modified "2023-10-05" @default.
- W3207712170 title "The type I interferonopathies: 10 years on" @default.
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