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- W3208091373 abstract "Saccharomyces cerevisiae, commonly known as baker's yeast, is one of the most comprehensively studied model organisms in science. Yeast has been used to study a wide variety of human diseases, and the yeast model system has proved to be an especially amenable tool for the study of lipids and lipid-related pathophysiologies, a topic that has gained considerable attention in recent years. This review focuses on how yeast has contributed to our understanding of the mitochondrial phospholipid cardiolipin (CL) and its role in Barth syndrome (BTHS), a genetic disorder characterized by partial or complete loss of function of the CL remodeling enzyme tafazzin. Defective tafazzin causes perturbation of CL metabolism, resulting in many downstream cellular consequences and clinical pathologies that are discussed herein. The influence of yeast research in the lipid-related pathophysiologies of Alzheimer's and Parkinson's diseases is also summarized." @default.
- W3208091373 created "2021-11-08" @default.
- W3208091373 creator A5013405117 @default.
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- W3208091373 creator A5017366259 @default.
- W3208091373 creator A5051052206 @default.
- W3208091373 creator A5075361012 @default.
- W3208091373 creator A5091068820 @default.
- W3208091373 date "2021-10-28" @default.
- W3208091373 modified "2023-10-14" @default.
- W3208091373 title "Studying Lipid-Related Pathophysiology Using the Yeast Model" @default.
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