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- W3208906877 endingPage "2867" @default.
- W3208906877 startingPage "2867" @default.
- W3208906877 abstract "Cystic fibrosis (CF) is the most common of rare hereditary diseases in Caucasians, and it is estimated to affect 75,000 patients globally. CF is a complex disease due to the multiplicity of mutations found in the CF transmembrane conductance regulator (CFTR) gene causing the CFTR protein to become dysfunctional. Correctors and potentiators have demonstrated good clinical outcomes for patients with specific gene mutations; however, there are still patients for whom those treatments are not suitable and require alternative CFTR-independent strategies. Although CFTR is the main chloride channel in the lungs, others could, e.g., anoctamin-1 (ANO1 or TMEM16A), compensate for the deficiency of CFTR. This review summarizes the current knowledge on calcium-activated chloride channel (CaCC) ANO1 and presents ANO1 as an exciting target in CF." @default.
- W3208906877 created "2021-11-08" @default.
- W3208906877 creator A5007768330 @default.
- W3208906877 creator A5026438946 @default.
- W3208906877 creator A5033744872 @default.
- W3208906877 creator A5037531874 @default.
- W3208906877 date "2021-10-24" @default.
- W3208906877 modified "2023-10-17" @default.
- W3208906877 title "TMEM16A/ANO1: Current Strategies and Novel Drug Approaches for Cystic Fibrosis" @default.
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