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- W4206711008 startingPage "176" @default.
- W4206711008 abstract "Autoimmune neuromuscular junction disorders are rare. However, myasthenia gravis is being increasingly recognised in people older than 50 years. In the past 5-10 years, epidemiological studies worldwide suggest an incidence of acetylcholine receptor antibody-positive myasthenia gravis of up to 29 cases per 1 million people per year. Muscle-specific tyrosine kinase antibody-positive myasthenia gravis and Lambert-Eaton myasthenic syndrome are about 20 times less common. Several diagnostic methods are available for autoimmune neuromuscular junction disorders, including serological antibody, electrophysiological, imaging, and pharmacological tests. The course of disease can be followed up with internationally accepted clinical scores or patient-reported outcome measures. For prognostic purposes, determining whether the disease is paraneoplastic is of great importance, as myasthenia gravis can be associated with thymoma and Lambert-Eaton myasthenic syndrome with small-cell lung cancer. However, despite well defined diagnostic parameters to classify patients into subgroups, objective biomarkers for use in the clinic or in clinical trials to predict the course of myasthenia gravis and Lambert-Eaton myasthenic syndrome are needed." @default.
- W4206711008 created "2022-01-26" @default.
- W4206711008 creator A5010743628 @default.
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- W4206711008 creator A5049165680 @default.
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- W4206711008 creator A5064459555 @default.
- W4206711008 date "2022-02-01" @default.
- W4206711008 modified "2023-10-10" @default.
- W4206711008 title "Epidemiology, diagnostics, and biomarkers of autoimmune neuromuscular junction disorders" @default.
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