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- W4210451063 endingPage "518" @default.
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- W4210451063 abstract "Primary Immune Regulatory Disorders (PIRD) are a newly recognized group of inborn errors of immunity (IEI) that are characterized by immune-mediated pathology ( Chan and Torgerson, 2020 ). Based on the genotype and phenotype, most PIRD fall into one of the following categories: T regulatory cell defects (also known as Tregopathies), autoinflammatory syndromes, nonmalignant lymphoproliferative disorders, interferonopathies, monogenic inflammatory bowel diseases (IBDs), and congenital atopic hypersensitivity. Some rheumatic diseases due to loss in self- tolerance can be considered PIRDs as well. Recognition of disease related manifestations of PIRD are crucial for prompt diagnosis and ensuing treatment of disease." @default.
- W4210451063 created "2022-02-08" @default.
- W4210451063 creator A5044959933 @default.
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- W4210451063 creator A5089607593 @default.
- W4210451063 date "2022-01-01" @default.
- W4210451063 modified "2023-10-18" @default.
- W4210451063 title "Above the Regular Tide: Primary Immune Regulatory Disorders (PIRD) Diagnosis and Treatment Considerations" @default.
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