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- W4210542986 endingPage "490" @default.
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- W4210542986 abstract "Genetic heart diseases are common causes of sudden cardiac death (SCD) in the young and are typically divided into inherited cardiomyopathies and primary electrical heart diseases. Cardiomyopathies associated with risk of SCD include hypertrophic cardiomyopathy (HCM) and arrhythmogenic cardiomyopathy (ACM). The latter includes arrhythmogenic right ventricular cardiomyopathy (ARVC) as well as ACM primarily affecting the left ventricle, such as lamin cardiomyopathy. Primary electrical diseases more commonly seen in clinical practice include Brugada syndrome (BrS) and long QT syndrome (LQTS). Risk stratification of SCD is a central component of the management of patients with these genetic heart diseases. Numerous risk factors have been identified with variable degrees of scientific evidence. More recently, risk prediction models have been developed to estimate the absolute risk of sustained arrhythmias and SCD, to support clinicians and patients in decision making regarding prophylactic implantable cardioverter-defibrillators (ICDs). This paper provides a practical review of the current literature on risk stratification in ARVC and other ACMs, HCM, BrS, and LQTS, and summarises current recommendations for ICD use." @default.
- W4210542986 created "2022-02-08" @default.
- W4210542986 creator A5026352242 @default.
- W4210542986 creator A5068211518 @default.
- W4210542986 date "2022-04-01" @default.
- W4210542986 modified "2023-09-27" @default.
- W4210542986 title "Predicting Sudden Cardiac Death in Genetic Heart Disease" @default.
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- W4210542986 doi "https://doi.org/10.1016/j.cjca.2022.01.025" @default.
- W4210542986 hasPubMedId "https://pubmed.ncbi.nlm.nih.gov/35108574" @default.
- W4210542986 hasPublicationYear "2022" @default.