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- W4211133311 endingPage "545" @default.
- W4211133311 startingPage "523" @default.
- W4211133311 abstract "Primary biliary cholangitis (PBC) is a cholestatic liver disease affecting predominantly middle-aged females, and which may progress to biliary cirrhosis if left untreated. Commonly reported symptoms include pruritus and fatigue, as well as symptoms of associated autoimmune conditions, such as xerostomia and xerophthalmia. The diagnosis is suspected in the presence of chronic unexplained elevation of serum alkaline phosphatase, and confirmed by a positive antimitochondrial antibody test and/or a consistent liver biopsy. Once the diagnosis is confirmed, treatment should be initiated with ursodeoxycholic acid (UDCA) 13-15 mg/kg per day; obeticholic acid 5-10 mg/day is now available for patients who are intolerant to, or who do not respond to UDCA. A minority of patients will progress to end-stage liver disease despite receiving treatment; liver transplantation is recommended for those patients, with excellent long-term patient and graft survival. Recurrence occurs in up to 40% of transplanted livers, but with little impact on survival." @default.
- W4211133311 created "2022-02-13" @default.
- W4211133311 creator A5002413555 @default.
- W4211133311 creator A5009192230 @default.
- W4211133311 creator A5060508119 @default.
- W4211133311 date "2017-10-23" @default.
- W4211133311 modified "2023-10-14" @default.
- W4211133311 title "Primary Biliary Cholangitis" @default.
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