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- W4213216813 abstract "Multiple endocrine neoplasia (MEN) is a group of heterogenous syndromes characterized by the occurrence of two or more endocrine gland tumors in a patient or related individuals in the same family. They are inherited in an autosomal dominant fashion and are highly penetrant. There are three types of MEN syndromes: MEN type 1 (MEN1), MEN type 2 (MEN2), and MEN type 4 (MEN4). MEN2 is further divided into MEN2A, MEN2B (formerly known MEN3), and familial medullary thyroid carcinoma (FMTC). Although MEN syndromes are rare, it is crucial to identify individuals at risk for potentially life-threatening neoplasias. This review article provides an update on each MEN syndrome, its genetics, diagnosis, and management in children." @default.
- W4213216813 created "2022-02-24" @default.
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- W4213216813 creator A5069120975 @default.
- W4213216813 date "2022-02-17" @default.
- W4213216813 modified "2023-09-30" @default.
- W4213216813 title "Multiple Endocrine Neoplasia in Childhood: An Update on Diagnosis, Screening, Management and Treatment" @default.
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