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- W4235370169 endingPage "17" @default.
- W4235370169 startingPage "2" @default.
- W4235370169 abstract "Abstract This review addresses several areas of concern in the care of patients with sickle cell disease. In Sections I and II, the fundamental pathogenetic mechanisms of sickle cell disease and their clinical consequences are discussed. Dr. Narla presents the evidence for abnormal cell adhesiveness by SS cells and Dr. Rosse examines the role of the increased whole blood viscosity. In Section III, Dr. Petz reviews common and uncommon alloimmune consequences of transfusion in sickle cell disease and discusses the diagnosis and management of sickle cell patients with hyperhemolysis after transfusion. In Section IV, Dr. Steinberg gives an update on the use of hydroxyurea in the treatment of sickle cell disease, including the SC and S-β thalassemia variants." @default.
- W4235370169 created "2022-05-12" @default.
- W4235370169 creator A5034746599 @default.
- W4235370169 creator A5068327377 @default.
- W4235370169 creator A5071776286 @default.
- W4235370169 creator A5074941406 @default.
- W4235370169 date "2000-01-01" @default.
- W4235370169 modified "2023-09-30" @default.
- W4235370169 title "New Views of Sickle Cell Disease Pathophysiology and Treatment" @default.
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- W4235370169 doi "https://doi.org/10.1182/asheducation.v2000.1.2.2" @default.