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- W4244848877 abstract "Mitochondria are double-membrane-enclosed organelles that ensure a number of central functions in the vast majority of eukaryotic cells. These include, among others, key steps in lipid and amino acid metabolism, biosynthesis of iron–sulfur clusters, heme, and further prosthetic groups, regulation of programmed cell death, and most prominently the final transformation of proteins, fats, and sugars into the cellular energy currency adenosine-5′-triphosphate (ATP) by oxidative phosphorylation (OXPHOS). Severe mitochondrial dysfunctions are associated with so-called mitochondrial diseases, and are largely associated with specific or broad OXPHOS defects. In addition, alterations of mitochondrial properties have been associated with other diseases associated with metabolic and/or physiologic alterations. This chapter aims to give a general introduction on mitochondrial properties and functions that will be further developed in subsequent chapters." @default.
- W4244848877 created "2022-05-12" @default.
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- W4244848877 date "2021-01-01" @default.
- W4244848877 modified "2023-10-14" @default.
- W4244848877 title "Mitochondria: Ultrastructure, dynamics, biogenesis, and main functions" @default.
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