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- W4298175868 abstract "The authors studied the somatosensory evoked potentials (SEPs) in 16 cases of myoclonic encephalopathies: 8 cases of dyssynergia cerebellaris myoclonica (DCM); 2 cases of dyssynergia cerebellaris progressiva (DCP); 2 cases of Lafora's disease; 1 case of ceroïd lipofuscinosis; 3 unclassifiable myoclonic syndromes.The mean age of the patients was 18 years and the mean duration of pre-study evolution was 10 years. All the patients had been treated by anticonvulsant drugs (phenobarbital, valproïc acid, benzodiazepines). The amplitude of the complex P1N2 at the level of the contralateral parietal cortex, with stimulation of the median nerve at the wrist, was found to be enlarged in only 6 cases and giant responses (over 40 μV) were obtained in 2 cases. Only half of the patients with DCM presented a high amplitude response. There was no correlation either with clinical parameters (and in particular, certain patients with marked action myoclonic jerks have a normal SEP), or with the EEG data: on the contrary, the amplitude variations of the SEPs are most often similar to variations of the visual evoked potentials.Les auteurs étudient les potentiels évoqués somesthésiques (PES) dans 16 cas d'encéphalopathies myocloniques: 8 cas de dyssynergie cérébelleuse myoclonique (DCM); 2 cas de dyssynergie cérébelleuse progressive (DCP); 2 cas de maladie de Lafora; 1 cas de céroïde-lipofuchsinose; 3 syndromes myocloniques inclassables.La moyenne d'âge des malades est de 18 ans et la durée moyenne d'évolution de la maladie est de 10 ans. Tous les malades ont été traités par des drogues anticomitiales (phénobarbital, acide valproïque, benzodiazépines). L'amplitude du complexe P1N2 au niveau du cortex pariétal controlatéral, avec stimulation du nerf médian au poignet, a été trouvée augmentée dans seulement 6 cas et des réponses géantes (supérieures à 40 μV) ont été obtenues dans 2 cas. Seulement la moitié des malades ayant une DCM présentent une réponse de grande amplitude. Il n'existe de corrélation ni avec les paramètres cliniques (et, en particulier, certains malades ayant d'importantes secousses myocloniques d'action ont un PES normal), ni avec les données de l'EEG; les variations d'amplitude des PES vont, par contre, le plus souvent dans le même sens que les variations des potentiels évoqués visuels." @default.
- W4298175868 created "2022-10-01" @default.
- W4298175868 date "1970-07-01" @default.
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- W4298175868 title "The EEG society" @default.
- W4298175868 doi "https://doi.org/10.1016/0013-4694(70)90088-x" @default.
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