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- W4308754595 endingPage "1868" @default.
- W4308754595 startingPage "1868" @default.
- W4308754595 abstract "Amyotrophic lateral sclerosis is a disease affecting upper and lower motor neurons. Although motor neuron death is the core event of ALS pathology, it is increasingly recognized that other tissues and cell types are affected in the disease, making potentially major contributions to the occurrence and progression of pathology. We review here the known cellular and molecular characteristics of muscle tissue affected by ALS. Evidence of toxicity in skeletal muscle tissue is considered, including metabolic dysfunctions, impaired proteostasis, and deficits in muscle regeneration and RNA metabolism. The role of muscle as a secretory organ, and effects on the skeletal muscle secretome are also covered, including the increase in secretion of toxic factors or decrease in essential factors that have consequences for neuronal function and survival." @default.
- W4308754595 created "2022-11-15" @default.
- W4308754595 creator A5006246228 @default.
- W4308754595 creator A5078187049 @default.
- W4308754595 creator A5080086156 @default.
- W4308754595 date "2022-11-08" @default.
- W4308754595 modified "2023-09-26" @default.
- W4308754595 title "The Cellular and Molecular Signature of ALS in Muscle" @default.
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