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- W4313246279 endingPage "326" @default.
- W4313246279 startingPage "326" @default.
- W4313246279 abstract "Diffuse parenchymal lung diseases (DPLD) or Interstitial lung diseases (ILD) are a heterogeneous group of lung conditions with common characteristics that can progress to fibrosis. Within this group of pneumonias, idiopathic pulmonary fibrosis (IPF) is considered the most common. This disease has no known cause, is devastating and has no cure. Chronic lesion of alveolar type II (ATII) cells represents a key mechanism for the development of IPF. ATII cells are specialized in the biosynthesis and secretion of pulmonary surfactant (PS), a lipid-protein complex that reduces surface tension and minimizes breathing effort. Some differences in PS composition have been reported between patients with idiopathic pulmonary disease and healthy individuals, especially regarding some specific proteins in the PS; however, few reports have been conducted on the lipid components. This review focuses on the mechanisms by which phospholipids (PLs) could be involved in the development of the fibroproliferative response." @default.
- W4313246279 created "2023-01-06" @default.
- W4313246279 creator A5013753779 @default.
- W4313246279 creator A5014214820 @default.
- W4313246279 creator A5018901039 @default.
- W4313246279 creator A5079382288 @default.
- W4313246279 date "2022-12-25" @default.
- W4313246279 modified "2023-10-13" @default.
- W4313246279 title "The Role of Pulmonary Surfactant Phospholipids in Fibrotic Lung Diseases" @default.
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