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- W4313472014 abstract "V poslednĂch letech dochĂĄzĂ k vĂ˝raznĂŠmu nĂĄrĹŻstu diagnostikovanĂ˝ch pĹĂpadĹŻ nemocnĂ˝ch s transthyretinovou amyloidĂłzou (ATTR) srdce, v naĹĄich podmĂnkĂĄch se zcela dominantnÄ jednĂĄ o zĂskanou formu ATTR (wtATTR, z angl. wildÂ‑type ATTR). Je to dĂĄno moĹžnostĂ neinvazivnĂ diagnostiky ATTR zaloĹženĂŠ na kombinaci jasnÄ pozitivnĂho nĂĄlezu pĹi scintigrafickĂŠm vyĹĄetĹenĂ bisfosfonĂĄty znaÄenĂ˝mi techneciem (nejÄastÄji DPD scintigrafie) a negativnĂm vĂ˝sledku laboratornĂch testĹŻ na AL amyloidĂłzu. Ukazuje se, Ĺže wtATTR nenĂ vzĂĄcnou pĹĂÄinou srdeÄnĂho selhĂĄnĂ Äi arytmiĂ, a to zejmĂŠna pĹevodnĂch poruch a fibrilace sĂnĂ, u starĹĄĂch nemocnĂ˝ch. CĂlem tohoto ÄlĂĄnku je proto poskytnout pĹehled klinickĂ˝ch manifestacĂ, diagnostickĂŠho procesu a moĹžnostĂ terapie ATTR vÄetnÄ jejĂ specifickĂŠ lĂŠÄby." @default.
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- W4313472014 date "2022-12-19" @default.
- W4313472014 modified "2023-09-30" @default.
- W4313472014 title "Transthyretin amyloidosis of the heart: Why should it be kept in mind?" @default.
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- W4313472014 doi "https://doi.org/10.36290/kar.2022.031" @default.
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