Matches in SemOpenAlex for { <https://semopenalex.org/work/W4316664554> ?p ?o ?g. }
- W4316664554 endingPage "213" @default.
- W4316664554 startingPage "213" @default.
- W4316664554 abstract "Since its discovery in 1955, the understanding of the lysosome has continuously increased. Once considered a mere waste removal system, the lysosome is now recognised as a highly crucial cellular component for signalling and energy metabolism. This notable evolution raises the need for a summarized review of the lysosome's biology. As such, throughout this article, we will be compiling the current knowledge regarding the lysosome's biogenesis and functions. The comprehension of this organelle's inner mechanisms is crucial to perceive how its impairment can give rise to lysosomal disease (LD). In this review, we highlight some examples of LD fine-tuned mechanisms that are already established, as well as others, which are still under investigation. Even though the understanding of the lysosome and its pathologies has expanded through the years, some of its intrinsic molecular aspects remain unknown. In order to illustrate the complexity of the lysosomal diseases we provide a few examples that have challenged the established single gene-single genetic disorder model. As such, we believe there is a strong need for further investigation of the exact abnormalities in the pathological pathways in lysosomal disease." @default.
- W4316664554 created "2023-01-17" @default.
- W4316664554 creator A5002144814 @default.
- W4316664554 creator A5003890565 @default.
- W4316664554 creator A5007884688 @default.
- W4316664554 creator A5015914439 @default.
- W4316664554 creator A5021782091 @default.
- W4316664554 creator A5077643807 @default.
- W4316664554 date "2023-01-14" @default.
- W4316664554 modified "2023-10-01" @default.
- W4316664554 title "The Biology of Lysosomes: From Order to Disorder" @default.
- W4316664554 cites W1413761512 @default.
- W4316664554 cites W1491957044 @default.
- W4316664554 cites W1498832295 @default.
- W4316664554 cites W1507640463 @default.
- W4316664554 cites W1509821238 @default.
- W4316664554 cites W1510849499 @default.
- W4316664554 cites W1782667879 @default.
- W4316664554 cites W1825944839 @default.
- W4316664554 cites W1900339045 @default.
- W4316664554 cites W1970661950 @default.
- W4316664554 cites W1975200363 @default.
- W4316664554 cites W1976514154 @default.
- W4316664554 cites W1977943960 @default.
- W4316664554 cites W1978527561 @default.
- W4316664554 cites W1979541893 @default.
- W4316664554 cites W1984065750 @default.
- W4316664554 cites W1984841297 @default.
- W4316664554 cites W1988003123 @default.
- W4316664554 cites W1993401680 @default.
- W4316664554 cites W1995692886 @default.
- W4316664554 cites W1996762971 @default.
- W4316664554 cites W1997861265 @default.
- W4316664554 cites W1998855132 @default.
- W4316664554 cites W2000678720 @default.
- W4316664554 cites W2001521415 @default.
- W4316664554 cites W2002845578 @default.
- W4316664554 cites W2004582874 @default.
- W4316664554 cites W2010538356 @default.
- W4316664554 cites W2011280194 @default.
- W4316664554 cites W2013589569 @default.
- W4316664554 cites W2014753621 @default.
- W4316664554 cites W2015126957 @default.
- W4316664554 cites W2017011727 @default.
- W4316664554 cites W2017593971 @default.
- W4316664554 cites W2017779665 @default.
- W4316664554 cites W2019946876 @default.
- W4316664554 cites W2025102169 @default.
- W4316664554 cites W2027797630 @default.
- W4316664554 cites W2035950274 @default.
- W4316664554 cites W2038049117 @default.
- W4316664554 cites W2042710439 @default.
- W4316664554 cites W2046447620 @default.
- W4316664554 cites W2052542184 @default.
- W4316664554 cites W2059052368 @default.
- W4316664554 cites W2060602529 @default.
- W4316664554 cites W2062172017 @default.
- W4316664554 cites W2062790216 @default.
- W4316664554 cites W2065734345 @default.
- W4316664554 cites W2069274491 @default.
- W4316664554 cites W2070658923 @default.
- W4316664554 cites W2071631353 @default.
- W4316664554 cites W2072471477 @default.
- W4316664554 cites W2073679788 @default.
- W4316664554 cites W2077326100 @default.
- W4316664554 cites W2077499130 @default.
- W4316664554 cites W2079133058 @default.
- W4316664554 cites W2082637970 @default.
- W4316664554 cites W2083270783 @default.
- W4316664554 cites W2089486887 @default.
- W4316664554 cites W2091599508 @default.
- W4316664554 cites W2092096150 @default.
- W4316664554 cites W2092678405 @default.
- W4316664554 cites W2098259366 @default.
- W4316664554 cites W2109716633 @default.
- W4316664554 cites W2111444310 @default.
- W4316664554 cites W2116505693 @default.
- W4316664554 cites W2116572569 @default.
- W4316664554 cites W2118597788 @default.
- W4316664554 cites W2118611462 @default.
- W4316664554 cites W2124663723 @default.
- W4316664554 cites W2125738893 @default.
- W4316664554 cites W2125999465 @default.
- W4316664554 cites W2127513771 @default.
- W4316664554 cites W2128073840 @default.
- W4316664554 cites W2132218390 @default.
- W4316664554 cites W2148351021 @default.
- W4316664554 cites W2149463340 @default.
- W4316664554 cites W2153824991 @default.
- W4316664554 cites W2156144699 @default.
- W4316664554 cites W2157272365 @default.
- W4316664554 cites W2157973824 @default.
- W4316664554 cites W2158028339 @default.
- W4316664554 cites W2159042370 @default.
- W4316664554 cites W2159362168 @default.
- W4316664554 cites W2162087993 @default.
- W4316664554 cites W2168360177 @default.
- W4316664554 cites W2179039419 @default.