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- W4322501851 endingPage "4602" @default.
- W4322501851 startingPage "4602" @default.
- W4322501851 abstract "Despite the significant progress that has been made in terms of understanding the pathophysiology and risk factors of Hirschsprung-associated enterocolitis (HAEC), the morbidity rate has remained unsatisfactorily stable, and clinical management of the condition continues to be challenging. Therefore, in the present literature review, we summarized the up-to-date advances that have been made regarding basic research on the pathogenesis of HAEC. Original articles published between August 2013 and October 2022 were searched in a number of databases, including PubMed, Web of Science, and Scopus. The keywords “Hirschsprung enterocolitis”, “Hirschsprung’s enterocolitis”, “Hirschsprung’s-associated enterocolitis”, and “Hirschsprung-associated enterocolitis” were selected and reviewed. A total of 50 eligible articles were obtained. The latest findings of these research articles were grouped into gene, microbiome, barrier function, enteric nervous system, and immune state categories. The present review concludes that HAEC is shown to be a multifactorial clinical syndrome. Only deep insights into this syndrome, with an accrual of knowledge in terms of understanding its pathogenesis, will elicit the necessary changes that are required for managing this disease." @default.
- W4322501851 created "2023-02-28" @default.
- W4322501851 creator A5005994478 @default.
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- W4322501851 creator A5066102428 @default.
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- W4322501851 creator A5087210747 @default.
- W4322501851 date "2023-02-27" @default.
- W4322501851 modified "2023-10-15" @default.
- W4322501851 title "Update on the Pathogenesis of the Hirschsprung-Associated Enterocolitis" @default.
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- W4322501851 doi "https://doi.org/10.3390/ijms24054602" @default.
- W4322501851 hasPubMedId "https://pubmed.ncbi.nlm.nih.gov/36902033" @default.