Matches in SemOpenAlex for { <https://semopenalex.org/work/W4366280060> ?p ?o ?g. }
- W4366280060 endingPage "441" @default.
- W4366280060 startingPage "421" @default.
- W4366280060 abstract "Primary cilia, antenna-like sensory organelles protruding from the surface of most vertebrate cell types, are essential for regulating signalling pathways during development and adult homeostasis. Mutations in genes affecting cilia cause an overlapping spectrum of >30 human diseases and syndromes, the ciliopathies. Given the immense structural and functional diversity of the mammalian cilia repertoire, there is a growing disconnect between patient genotype and associated phenotypes, with variable severity and expressivity characteristic of the ciliopathies as a group. Recent technological developments are rapidly advancing our understanding of the complex mechanisms that control biogenesis and function of primary cilia across a range of cell types and are starting to tackle this diversity. Here, we examine the structural and functional diversity of primary cilia, their dynamic regulation in different cellular and developmental contexts and their disruption in disease." @default.
- W4366280060 created "2023-04-20" @default.
- W4366280060 creator A5044711408 @default.
- W4366280060 creator A5048497534 @default.
- W4366280060 creator A5052259427 @default.
- W4366280060 date "2023-04-18" @default.
- W4366280060 modified "2023-10-18" @default.
- W4366280060 title "Primary cilia as dynamic and diverse signalling hubs in development and disease" @default.
- W4366280060 cites W1504068681 @default.
- W4366280060 cites W1588994353 @default.
- W4366280060 cites W1680718768 @default.
- W4366280060 cites W1900540592 @default.
- W4366280060 cites W1954666599 @default.
- W4366280060 cites W1970264904 @default.
- W4366280060 cites W1970799181 @default.
- W4366280060 cites W1971197630 @default.
- W4366280060 cites W1976421227 @default.
- W4366280060 cites W1976989450 @default.
- W4366280060 cites W1981137206 @default.
- W4366280060 cites W1982168739 @default.
- W4366280060 cites W1985225356 @default.
- W4366280060 cites W1989248251 @default.
- W4366280060 cites W1989506884 @default.
- W4366280060 cites W1990577046 @default.
- W4366280060 cites W1995140705 @default.
- W4366280060 cites W1997989369 @default.
- W4366280060 cites W1999701778 @default.
- W4366280060 cites W2001372249 @default.
- W4366280060 cites W2002153732 @default.
- W4366280060 cites W2005619876 @default.
- W4366280060 cites W2011450474 @default.
- W4366280060 cites W2023564722 @default.
- W4366280060 cites W2026335052 @default.
- W4366280060 cites W2029279705 @default.
- W4366280060 cites W2030939638 @default.
- W4366280060 cites W2031584736 @default.
- W4366280060 cites W2032002501 @default.
- W4366280060 cites W2032792789 @default.
- W4366280060 cites W2033799985 @default.
- W4366280060 cites W2035327107 @default.
- W4366280060 cites W2038678925 @default.
- W4366280060 cites W2041656617 @default.
- W4366280060 cites W2041964741 @default.
- W4366280060 cites W2054954402 @default.
- W4366280060 cites W2055910256 @default.
- W4366280060 cites W2061103085 @default.
- W4366280060 cites W2062938087 @default.
- W4366280060 cites W2064736720 @default.
- W4366280060 cites W2068918824 @default.
- W4366280060 cites W2070184849 @default.
- W4366280060 cites W2073256310 @default.
- W4366280060 cites W2076640448 @default.
- W4366280060 cites W2079380806 @default.
- W4366280060 cites W2081393679 @default.
- W4366280060 cites W2082188981 @default.
- W4366280060 cites W2082683558 @default.
- W4366280060 cites W2091684557 @default.
- W4366280060 cites W2099008080 @default.
- W4366280060 cites W2103377139 @default.
- W4366280060 cites W2106682048 @default.
- W4366280060 cites W2110772590 @default.
- W4366280060 cites W2111356783 @default.
- W4366280060 cites W2112200758 @default.
- W4366280060 cites W2113283367 @default.
- W4366280060 cites W2114339744 @default.
- W4366280060 cites W2114819889 @default.
- W4366280060 cites W2118640963 @default.
- W4366280060 cites W2119016119 @default.
- W4366280060 cites W2123700457 @default.
- W4366280060 cites W2133192672 @default.
- W4366280060 cites W2134267863 @default.
- W4366280060 cites W2136002176 @default.
- W4366280060 cites W2136445329 @default.
- W4366280060 cites W2136881701 @default.
- W4366280060 cites W2137065610 @default.
- W4366280060 cites W2138374168 @default.
- W4366280060 cites W2140600466 @default.
- W4366280060 cites W2140864413 @default.
- W4366280060 cites W2141570562 @default.
- W4366280060 cites W2144225452 @default.
- W4366280060 cites W2151072513 @default.
- W4366280060 cites W2159407840 @default.
- W4366280060 cites W2160084509 @default.
- W4366280060 cites W2162787110 @default.
- W4366280060 cites W2171652940 @default.
- W4366280060 cites W2173846013 @default.
- W4366280060 cites W2177564588 @default.
- W4366280060 cites W2198245530 @default.
- W4366280060 cites W2207677128 @default.
- W4366280060 cites W2290993632 @default.
- W4366280060 cites W2291971412 @default.
- W4366280060 cites W2292239198 @default.
- W4366280060 cites W2310131378 @default.
- W4366280060 cites W2312564601 @default.
- W4366280060 cites W2320051121 @default.
- W4366280060 cites W2327512461 @default.
- W4366280060 cites W2338378167 @default.
- W4366280060 cites W2346539852 @default.