Matches in SemOpenAlex for { <https://semopenalex.org/work/W4366609766> ?p ?o ?g. }
- W4366609766 endingPage "244" @default.
- W4366609766 startingPage "236" @default.
- W4366609766 abstract "The clinical management of autosomal dominant polycystic kidney disease (ADPKD) in adults has shifted from managing complications to delaying disease progression through newly emerging therapies. Regarding pediatric management of the disease, there are still specific hurdles related to the management of children and adolescents with ADPKD and, unlike adults, there are no specific therapies for pediatric ADPKD or stratification models to identify children and young adults at risk of rapid decline in kidney function. Therefore, early identification and management of factors that may modify disease progression, such as hypertension and obesity, are of most importance for young children with ADPKD. Many of these risk factors could promote disease progression in both ADPKD and chronic kidney disease. Hence, nephroprotective measures applied early in life can represent a window of opportunity to prevent the decline of the glomerular filtration rate especially in young patients with ADPKD. In this review, we highlight current challenges in the management of patients with pediatric ADPKD, the importance of early modifying factors in disease progression as well as the gaps and future perspectives in the pediatric ADPKD research field." @default.
- W4366609766 created "2023-04-23" @default.
- W4366609766 creator A5041078525 @default.
- W4366609766 creator A5064202053 @default.
- W4366609766 creator A5064880288 @default.
- W4366609766 date "2023-05-01" @default.
- W4366609766 modified "2023-10-07" @default.
- W4366609766 title "Autosomal Dominant Polycystic Kidney Disease in Children and Adolescents: Assessing and Managing Risk of Progression" @default.
- W4366609766 cites W1924478590 @default.
- W4366609766 cites W1964562911 @default.
- W4366609766 cites W1982151472 @default.
- W4366609766 cites W1983789728 @default.
- W4366609766 cites W1985685880 @default.
- W4366609766 cites W1991469478 @default.
- W4366609766 cites W1992064700 @default.
- W4366609766 cites W1997286719 @default.
- W4366609766 cites W2003478839 @default.
- W4366609766 cites W2012159432 @default.
- W4366609766 cites W2012933903 @default.
- W4366609766 cites W2014173460 @default.
- W4366609766 cites W2017871510 @default.
- W4366609766 cites W2018718574 @default.
- W4366609766 cites W2024394081 @default.
- W4366609766 cites W2026415637 @default.
- W4366609766 cites W2030104772 @default.
- W4366609766 cites W2030927065 @default.
- W4366609766 cites W2034578084 @default.
- W4366609766 cites W2041227924 @default.
- W4366609766 cites W2047999066 @default.
- W4366609766 cites W2054205416 @default.
- W4366609766 cites W2055448210 @default.
- W4366609766 cites W2055919784 @default.
- W4366609766 cites W2067420164 @default.
- W4366609766 cites W2074616461 @default.
- W4366609766 cites W2075391935 @default.
- W4366609766 cites W2075557271 @default.
- W4366609766 cites W2096587435 @default.
- W4366609766 cites W2101067234 @default.
- W4366609766 cites W2101166125 @default.
- W4366609766 cites W2107867025 @default.
- W4366609766 cites W2111053427 @default.
- W4366609766 cites W2112643254 @default.
- W4366609766 cites W2116811919 @default.
- W4366609766 cites W2118184386 @default.
- W4366609766 cites W2119890307 @default.
- W4366609766 cites W2120581740 @default.
- W4366609766 cites W2136124373 @default.
- W4366609766 cites W2143108257 @default.
- W4366609766 cites W2151157805 @default.
- W4366609766 cites W2152162813 @default.
- W4366609766 cites W2152628928 @default.
- W4366609766 cites W2154355204 @default.
- W4366609766 cites W2156473928 @default.
- W4366609766 cites W2162269191 @default.
- W4366609766 cites W2166766512 @default.
- W4366609766 cites W2169620365 @default.
- W4366609766 cites W2189612961 @default.
- W4366609766 cites W2214691690 @default.
- W4366609766 cites W2240703978 @default.
- W4366609766 cites W2288972352 @default.
- W4366609766 cites W2318270239 @default.
- W4366609766 cites W2332684753 @default.
- W4366609766 cites W2414499905 @default.
- W4366609766 cites W2467017262 @default.
- W4366609766 cites W2512143173 @default.
- W4366609766 cites W2577378324 @default.
- W4366609766 cites W2740475263 @default.
- W4366609766 cites W2765795120 @default.
- W4366609766 cites W2766704070 @default.
- W4366609766 cites W2768047744 @default.
- W4366609766 cites W2776384152 @default.
- W4366609766 cites W2781941362 @default.
- W4366609766 cites W2794019957 @default.
- W4366609766 cites W2799298579 @default.
- W4366609766 cites W2887422854 @default.
- W4366609766 cites W2888346415 @default.
- W4366609766 cites W2902654232 @default.
- W4366609766 cites W2904572145 @default.
- W4366609766 cites W2922417801 @default.
- W4366609766 cites W2929633637 @default.
- W4366609766 cites W2942607819 @default.
- W4366609766 cites W2945797083 @default.
- W4366609766 cites W2947194217 @default.
- W4366609766 cites W2959265564 @default.
- W4366609766 cites W2994090564 @default.
- W4366609766 cites W3008794440 @default.
- W4366609766 cites W3016276823 @default.
- W4366609766 cites W3034052252 @default.
- W4366609766 cites W3040659673 @default.
- W4366609766 cites W3118299378 @default.
- W4366609766 cites W3133814581 @default.
- W4366609766 cites W3135355396 @default.
- W4366609766 cites W3176251154 @default.
- W4366609766 cites W3185139843 @default.
- W4366609766 cites W3192198801 @default.
- W4366609766 cites W3216331483 @default.
- W4366609766 cites W333845133 @default.
- W4366609766 cites W4200177974 @default.